Introduction to Biliary Atresia

Introduction to Biliary Atresia

Nio, Masaki

Springer Verlag, Singapore

07/2021

350

Dura

Inglês

9789811621598

15 a 20 dias

1281

Descrição não disponível.
Biliary Atresia: A Historical Overview.- History of The Japanese Biliary Atresia Society (JABS).- Japanese Biliary Atresia Registry (JBAR).- Pathogenesis: Overview.- Pathogenesis: Genetics/Epigenetics.- Pathogenesis: Viral Infection.- Pathogenesis: Maternal Microchimerism.- Epidemiology: Incidence and Gender Ratio.- Epidemiology: Ethnic Variations/Family Histories/Heredity.- Epidemiology: Gestational Age/Birth Weight /Associated Anomalies.- Classifications.- Mass Screening.- Stool Color Card System.- Prenatal Diagnosis and Signs/Symptoms.- Intracranial Hemorrhage.- Pathology.- Biomarkers.- Differential Diagnosis.- Diagnostic Modalities.- Preoperative Management and Direct Cholangiography.- Operative Procedures: Open Kasai Procedure.- Operative Procedures: Laparoscopic Kasai Procedure.- Operative Procedures: Re-do Kasai Procedure.- Operative Procedures: Cadaveric Liver Transplantation.- Operative Procedures: Living Donor Liver Transplantation.- Medical Treatment: UDCA/Steroid.- MedicalTreatment: Kampo Medicine.- Prevention/Treatment of Postoperative Cholangitis.- Nutritional Support.- Protocols of Follow-up Management.- Prognostic Indicators.- Long-term Complications: Gastro-Esophageal Varices.- Long-term Complications: Hypersplenism.- Long-term Complications: Cholangitis/Gall Stones.- Long-term Complications: Hepatopulmonary Syndrome.- Long-term Complications: Portopulmonary Hypertension.- Long-term Complications: Liver Cirrhosis/Hepatic Encephalopathy.- Long-Term Results, General.- Long-Term Results, Deformity of Intrahepatic Bile Ducts.- Long-Term Results, Social Performance.- Long-Term Results, Liver Transplantation.- Biliary Atresia and Pregnancy/Delivery.- Biliary Atresia and Malignancy.- Future Prospects.- Transition in Biliary Atresia.- Society of Patients and Families.- Clinical Guidelines for Biliary Atresia.
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Biliary atresia;Pathogenesis;Epidemiology;Portoenterostomy;Postoperative care;Long-term follow-up;Biomarker;Diagnostic Modality;hepatology